Helicoidal peripapillary chorioretinal degeneration: electrophysiology and psychophysics in 17 patients
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منابع مشابه
Helicoidal peripapillary chorioretinal degeneration: electrophysiology and psychophysics in 17 patients.
AIMS To characterise retinal function using electrophysiological and psychophysical tests in 17 patients with helicoidal peripapillary chorioretinal degeneration. METHODS The electroretinogram (ERG) was recorded using gold foil corneal electrodes. The electro-oculogram (EOG) was recorded using a standard protocol. Dark adaptometry was recorded with an SST-1 dark adaptometer and colour vision ...
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Abetalipoproteinemia is a rare autosoma1 recessive disorder characterized by the absence of apolipoprotein B.' It is caused by mutations of the microsomal triglyceridetransfer protein gene.' Ocular manifestations include retinitis pigmentosa-like changes, nystagmus, ophthalmoplegia, ptosis, cataracts, anisocoria, and angioid ~treaks.~ Helicoid peripapillary chorioretinal degeneration (HPCD) is ...
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Sveinsson's chorioretinal atrophy (SCRA), also referred to as helicoid peripapillary chorioretinal degeneration or atrophia areata, is an autosomal dominant eye disease, characterized by symmetrical lesions radiating from the optic disc involving the retina and the choroid. Genome-wide linkage analysis mapped the SCRA gene to chromosome 11p15 in 81 patients from a large founder pedigree in Icel...
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We investigate the form and time course of motion adaptation, comparing the psychophysical performance of human subjects with existing electrophysiological data on insect vision. In the H1 neuron of the fly, the response to a maintained motion stimulus is known to decrease over time while sensitivity to variations in speed around the maintained level increases. This behaviour can be modelled by...
متن کاملKinetics of foveal cone photopigment in myopia without chorioretinal degeneration.
PURPOSE To study the early changes in the outer retina of myopic eyes, we performed fundus reflection foveal cone densitometry in 45 subjects with normal visual acuity and no chorioretinal degeneration (ages: 18-47 years, refraction; +2.00-(-14.50) diopters). METHODS After full bleaching, the density of the photopigment was measured for 7 minutes by using a test spot, 562 nm in wavelength and...
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ژورنال
عنوان ژورنال: British Journal of Ophthalmology
سال: 1998
ISSN: 0007-1161
DOI: 10.1136/bjo.82.3.280